Infantile myofibromatosis*

نویسندگان

  • Margarita Larralde
  • Bruno Ferrari
  • Juan Pablo Martinez
  • María Angélica Fernández Barbieri
  • José Higinio Méndez
  • José Casas
چکیده

Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.

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عنوان ژورنال:

دوره 92  شماره 

صفحات  -

تاریخ انتشار 2017